Compartir
Publique en esta revista
Información de la revista

Congreso

Contenidos del congreso
Congreso
XXI Congreso Nacional de la Sociedad Española de Neurocirugía
Barcelona, 17-19 Mayo 2017
Listado de sesiones
Comunicación
Texto completo

C0476 - LHERMITTE-DUCLOS DISEASE OR CEREBELLAR DYSPLASTIC GANGLIOCYTOMA

Y. Kacar, M.I. Ozer, C. Kural, R. Mehtiyev, M.C. Ezgu and Y. Izci

Gulhane Egitim Ve Arastirma Hastanesi Kecioren, Ankara, Turkey.

Objectives: Lhermitte-Duclos disease is a rare autosomal recessive disease. We present a 6-year-old child patient who has been diagnosed with Lhermitte-Duclos in our clinic.

Methods: 6-year-old child with congenital Erb-Fallen paralysis, applied with headache to our clinic. Right cerebellar mass was found on MRI due to headache. MRI has been reported as a low-grade glial tumor. The lesion is microscopically gross total excised with right suboccipital craniotomy.

Results: Frozen section result was reported as normal cerebellar tissue during surgery. Histopathological result were reported microscopically and immunohistochemically as Lhermitte-Duclos. Focal hyperplasia of the cerebellar cortex is seen as pathological feature. Asymmetric growth of the cerebellum and also sharp thickening and condensation are observed in affected Gyrus macroscopically.on the other hand Condensation is observed in neurons similar to Purkinje cells with broad cytoplasm in the granular layer of the cerebellar cortex as microscopically.

Conclusions: Lhermitte-Duclos is a rare and slow progressive disease, generally seen in adolescence or in 3-4 decades. Early diagnosis and surgical treatment increase survival in these patients.

Idiomas
Neurocirugía

Suscríbase al Newsletter

Política de cookies
Utilizamos cookies propias y de terceros para mejorar nuestros servicios y mostrarle publicidad relacionada con sus preferencias mediante el análisis de sus hábitos de navegación. Si continua navegando, consideramos que acepta su uso. Puede cambiar la configuración u obtener más información aquí.